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Summary Expression Phenotypes Gene Literature (1) GO Terms (44) Nucleotides (115) Proteins (41) Interactants (236) Wiki
XB-GENEPAGE-1013274
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 lonp1

???displayGene.name???: 
lon peptidase 1, mitochondrial

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( Nomenclature history )

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Mitochondrial ATP-dependent protease PIM1/LON

AI Protein Function :
The lonp1 gene encodes a mitochondrial protease atpase belonging to the aaa+ superfamily. The encoded protein localizes to the mitochondrial matrix where it facilitates protein quality control through ...[+]


InterPro :
ATPase AAA core, Peptidase S16 AS, Ribosomal S5 D2-typ fold, PUA-like sf, [+]

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Diseases: 


Disease Ontology:
CODAS syndrome

MIM:
CODAS SYNDROME

External Links:
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???displayGene.expression???                  Development Stages                                               Embryonic Tissues                                                                Adult Tissues
More Information
Xenbase Expression Details In situ images Single cell data at SPRING In situ: RNA-Seq:


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